Home >> Archive >>Vol:1, No:2>>Partial Thoracic Type Ectopia Cordis; a Case Report

Partial Thoracic Type Ectopia Cordis; a Case Report

| Tugay Tepe | | Mustafa Özdemir | | Şerif Hamitoğlu | | Ahmet Kurtoğlu | | Hacer Yapıcıoğlu | | Ferda Özlü | | Orhan Kemal Salih | | Eyüphan Gencel | | Ömer Kokaçya | | Anıl Atmış | | Nejat Narlı | | Mehmet Satar |

Year: 2022 | Vol: 1 | No: 2 | PP 69-77

Ectopia Cordis (EC) is defined as a congenital defect which babies are born with their hearts outside their bodies. Abnormally located hearth (partially or totally outside of the thorax) mostly causes accompanying congenital anomalies. Although treatment options are limited and mortality rate is relatively high, surgical intervention is one of the most common treatment approaches. This paper presents a case of thoracic ectopia cordis with good outcome and its surgical intervention.

Ectopia Cordis; Surgery; Case; Intervention
Full Paper (PDF)

Rights and permissions
Creative Commons License
This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. According to Creative Commons: This license allows reusers to copy and distribute the material in any medium or format in unadapted form only, for noncommercial purposes only, and only so long as attribution is given to the creator.

  1. Cantrell, J. R; Haller, J A.; Ravitch, MM and thers, A syndrome of congenital defects involving the abdominal wall, sternum, diaphragm, pericardium, and heart. In Surg Gynecol Obstet, 107 (5): 602-614, 1958.
  2. Harrison, M. R; Filly, R. A; Stanger, P. and de Lorimier, A. A Prenatal diagnosis and management of omphalocele and ectopia cordis. In Journal of pediatric surgery, 17 (1): 64-66, 1982.
  3. Pamidi, N.; Vollala, V. R; Nayak, S. and Bhat, S. Ectopia cordis and amniotic band syndrome. In Archives of Medical Science, 4 (2): 208-211, 2008.
  4. Humpl, T.; Huggan, P.; Hornberger, L. K and McCrindle, B. W Presentation and outcomes of ectopia cordis. In The Canadian Journal of Cardiology, 15 (12): 1353-1357, 1999.
  5. Dobell, A.; Williams, HB and Long, RW Staged repair of ectopia cordis. In Journal of pediatric surgery, 17 (4): 353-358, 1982.
  6. Kaplan, L. C; Matsuoka, R.; Gilbert, E. F; Opitz, J. M; Kurnit, D. M and Reynolds, J. F Ectopia cordis and cleft sternum: evidence for mechanical teratogenesis following rupture of the chorion or yolk sac. In American journal of medical genetics, 21 (1): 187-199, 1985.
  7. Achiron, R; Shimmel, M; Farber, B and Glaser, J Prenatal sonographic diagnosis and perinatal management of ectopia cordis. In Ultrasound in Obstetrics and Gynecology: The Official Journal of the International Society of Ultrasound in Obstetrics and Gynecology, 1 (6): 431-434, 1991.
  8. Kanagasuntheram, R and Verzin, JA Ectopia cordis in man. In Thorax, 17 (2): 159, 1962.
  9. Puvabanditsin, S.; Di Stefano, V.; Garrow, E.; Wong, R.; Eng, J. and Balbin, J. Ectopia cordis. In Hong Kong Med J, 19 (5): 447-50, 2013.
  10. Engum, S. A Embryology, sternal clefts, ectopia cordis, and Cantrell's pentalogy. In Seminars in pediatric surgery, pages 154-160, 2008.
  11. Smith, B. J; Flyer, J. N; Edwards, E. M; Soll, R. F; Horbar, J. D and Yeager, S. B Outcomes for Ectopia Cordis. In The Journal of Pediatrics, 216: 67-72, 2020.
  12. Carmi, R; Parvari, R; Ehrlich, S; Cwikel, B and Weinstein, Y Mapping of an X-linked gene for ventral midline defects (the TAS gene). In Birth defects original article series, 30 (1): 179-187, 1996.
  13. Hannoun, A.; Usta, I. M; Sawaya, F. and Nassar, A. H First trimester sonographic diagnosis of ectopia cordis: a case report and review of the literature. In The Journal of Maternal-Fetal & Neonatal Medicine, 24 (6): 867-869, 2011.
  14. Sadlecki, P.; Krekora, M.; Krasomski, G.; Walentowicz-Sadlecka, M.; Grabiec, M.; Moll, J. and Respondek-Liberska, M. Prenatally evolving ectopia cordis with successful surgical treatment. In Fetal diagnosis and therapy, 30 (1): 70-72, 2011.